Is fibromatosis a malignant tumor?
Desmoid tumor is called aggressive fibromatosis as it has similarities with a malignant (cancerous) tumor called fibrosarcoma. However, it is considered benign because it does not metastasize (spread) to other parts of the body.
What is abdominal fibromatosis?
Abdominal fibromatosis is a condition characterised by benign soft tissue tumours on the abdominal wall. Although they are not malignant and cannot spread to other parts of the body, they can grow rather aggressively and invade abdominal organs.
What type of cancer is fibromatosis?
Desmoid tumors or aggressive fibromatosis are classified as benign tumors because of their lack of metastatic potential and low risk of mortality.
Is fibromatosis serious?
Head and neck desmoid fibromatosis is a serious condition due to local aggression, specific anatomical patterns and the high rate of relapse. For children surgery is particularly difficult, given the potential for growth disorders. Treatment includes prompt radical excision with a wide margin and/or radiation.
What is the treatment for fibromatosis?
Treatment options include surgery, nonsteroidal anti-inflammatory drugs with or without hormonal manipulation, chemotherapy, radiation therapy, and other forms of local therapy. Many treatments have been used, but these are not without toxicities.
What is fibromatosis tumor?
Desmoid tumors are also known as aggressive fibromatosis or desmoid-type fibromatosis. A desmoid tumor can occur anywhere in the body since connective tissue is found everywhere in your body. Desmoid tumors are often found in the abdomen, as well as the shoulders, upper arms, and thighs.
Are desmoid tumors fatal?
Desmoid tumors are usually considered benign (not cancer) because they rarely spread to different parts of your body. But ones that grow fast (aggressive tumors) can be like cancer in some ways. They can grow into nearby tissues and can be fatal. These tumors can grow almost anywhere in your body and at any age.
Is fibromatosis curable?
There is no cure for desmoid tumors; when possible, patients are encouraged to enlist in clinical trials. A biopsy is always indicated as the definitive method to determine nature of the tumour. Management of these lesions is complex, the main problem being the high rates of recurrence in FAP associated disease.
What is the cause of fibromatosis?
What causes fibromatosis? The cause of fibromatosis remains unclear. In some types of fibromatosis such as desmoid tumours, it is thought that the condition may be related to trauma, hormonal factors, or have a genetic association.
When does inflammatory myofibroblastic tumor occur in children?
Although the tumor may occur at any age, inflammatory myofibroblastic tumor most commonly affects children and young adults, with a slight tendency to occur more frequently in girls ( 6, 11, 12 ). The clinical symptoms of inflammatory myofibroblastic tumor are nonspecific and variable, depending on the site of origin.
Can a child have an intraperitoneal solid tumor?
Intraperitoneal solid tumors are far less common in children than in adults, and the histologic spectrum of neoplasms of the peritoneum and its specialized folds in young patients differs from that in older patients.
Is there a difference between pediatric abdominal and pelvic tumors?
The differential diagnoses of pediatric abdominal and pelvic tumors arising in solid organs are generally well known, but the pathologic features of tumors originating outside these organs—from the peritoneum, omentum, and mesentery—is much less familiar.